Boost your Grades with us today!
You can get professional Cystic Fibrosis Nursing Assignment Help from our Essay For All experts. Cystic Fibrosis (CF) is an exocrine gland disease encompassing different organ systems. It results in chronic respiratory infections, pancreatic enzyme insufficiency, and other risk factors if left untreated. Thus, cystic fibrosis is an autosomal recessive disorder, with most carriers of this gene asymptomatic. The disease is an inherited disorder causing extreme damage to the lungs, digestive system, and other body organs.
Generally, this disorder affects mucus, sweat, and digestive juices-producing cells. In healthy individuals, secreted fluids are usually thin and watery. Unfortunately, this is not the situation with persons having a CF disorder. The secretive gene causes the secretions to become sticky and thick. As a result, these secreted fluids can no longer act as lubricants but instead plug up tubes, ducts, and passageways in the lungs and pancreas.
Cystic fibrosis is a progressive disorder. As a result, it requires routine care since persons suffering from this condition can continue their routine activities. Due to advancements in the medical field, individuals with the disorder have an enhanced life quality than in previous years. For example, statistics show that most can live up to their mid-thirties, while others can live for as long as forty years or more.
Cystic fibrosis is a genetic disease causing sticky, thick mucus to build up in body organs, such as the lungs and pancreas. Consequently, the thick mucus blocks the airway, making breathing difficult. Thus, it demands regular clearing of the lungs. The thick mucus also blocks the pancreatic duct, causing challenges with food digestion. Children and kids having the disorder cannot absorb sufficient nutrients from food into their bodies. The disorder progresses gradually to affect a person’s liver, sinuses, intestines, and sexual organs.
Cystic fibrosis causes
Statistics show that CF incidences in the United States occur in one out of every 3300 white children and in one out of every 16300 African American children. The approximated heterozygote frequency in white people is approximately one in every twenty persons. It is an autosomal disease caused by defects in the CFTR gene, encoding for protein functioning as a chloride channel in the body. CF disorder causes involve:
- CFTR mutations cause abnormalities in chloride transportation across the epithelial cells on the mucosal surfaces. Whenever this occurs, it results in viscid secretions in the respiratory tract, pancreas, sweat glands, GI tract, and various exocrine tissues
- Environmental factors also cause this disorder. For example, research shows that an incomplete correlation of genotype with phenotype shows either an environmental aspect of organ dysfunction or other modifying genes recently being classified. The role of these modifier genes relies on the understanding that neonates with cystic fibrosis with intestinal obstruction usually have abnormalities in two or more CFTR modifier genes
Furthermore, CF emanates from a gene mutation. Cystic fibrosis transmembrane conductance (CFTR) genes change the protein regulating salt movement in and out of the cells. This results in thick and sticky mucus in the respiratory, digestive, and reproductive systems. The condition is usually characterized by increased salt content in a person’s sweat. Genes can have multiple defects.
However, the gene mutation type relies on the condition’s severity. Children should inherit a single gene copy from each parent to have CF disorder. So, if they inherit only one copy, they will not develop the cystic disorder, but they can be carriers of the disorder and pass the gene to their children. The primary risk factor linked to this condition is its inherited trait. Therefore, it runs in families through a family history of CF disorder.
Cystic fibrosis symptoms and complications, as outlined by our Cystic Fibrosis Nursing Assignment Help tutors at Essay For All
Cystic fibrosis signs and symptoms vary depending on the condition’s severity. CF is a progressive chronic disease. This implies that the symptoms may worsen with time. For example, some people may experience the symptoms early, while others may appear later in their teenage years. In most cases, parents can ascertain the high salt content whenever they kiss their children. The signs and symptoms associated with this condition include the following:
- Respiratory signs and symptoms occur due to the thick and sticky mucus linked with the CF disorder because of the clogs in the tubes carrying air in and out of the lungs. The signs and symptoms include the following:
- Persistent cough producing thick mucus
- Exercise intolerance
- Consistent lung infections
- Inflamed nasal passages
Secondly, cystic fibrosis has digestive signs and symptoms since the thick sticky mucus can cause blockage of the tubes carrying digestive enzymes from your pancreas to the small intestine. Whenever this happens, your intestines cannot completely absorb nutrients in the food a person consumes due to a lack of digestive enzymes.
The digestive symptoms include the following:
- Low-quality weight gain and growth
- Intestinal blockage in newborns
- Foul-smelling and greasy stool
- Chronic and severe constipation characterized by extreme straining while training to pass stool. This can cause some parts of the rectum to protrude outside the anus
Cystic fibrosis also has different complications due to the strains and the blockage it causes. This can affect the respiratory, digestive, and reproductive systems. Some of the complications include the following:
- The first CF disorder complication is damage to the airways. Studies show that cystic fibrosis is the leading cause of bronchiectasis, a lung condition with abnormal widening and scarring of the airways. This makes it difficult for air to move in and out of the lungs. In addition, it makes it impossible to clear the mucus from the bronchiole tubes
- Secondly, it can cause chronic infections because of the thick mucus in the lungs and sinuses. Generally, the thick mucus provides a breeding ground for bacteria and fungi to do their activities.
- Nasal polyps are another complication associated with this condition. The lining inside the nose becomes inflamed and swollen, leading to the development of soft and fleshy growths
Cystic fibrosis management, as outlined by our Cystic Fibrosis Nursing Assignment Helpers at Essay For All
The adverse impacts of CF disorder require prompt measures. The nursing care planning goals for this condition aim at the following:
- Relieving immediate respiratory distress
- Ensuring adequate oxygenation of the lungs
- Protecting the body from possible complications and infections
- Enhancing a patient’s nutritional status
- Relieving anxiety
For this reason, medications used to treat CF disorder include pancreatic enzyme supplements, fat-soluble vitamins, antibiotics, inhaled and oral antibiotics, bronchodilators, anti-inflammatory agents, and CFRT potentiates.
Other services offered under our assignment help include
- Osteoarthritis Nursing Assignment Help
- Otitis Media Nursing Assignment Help
- Otolaryngology Nursing Assignment Help
- Ovarian Cancer Nursing Assignment Help
- CV Imaging Nursing Assignment Help